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001 978-0-387-84847-1
003 DE-He213
005 20251006084423.0
007 cr nn 008mamaa
008 100301s2008 xxu| s |||| 0|eng d
020 _a9780387848471
020 _a99780387848471
024 7 _a10.1007/978-0-387-84847-1
_2doi
082 0 4 _a610
_223
100 1 _aLaing, Nigel G.
_eeditor.
245 1 4 _aThe Sarcomere and Skeletal Muscle Disease
_h[electronic resource] /
_cedited by Nigel G. Laing.
264 1 _aNew York, NY :
_bSpringer New York,
_c2008.
300 _aXXII, 228 p.
_bonline resource.
336 _atext
_btxt
_2rdacontent
337 _acomputer
_bc
_2rdamedia
338 _aonline resource
_bcr
_2rdacarrier
347 _atext file
_bPDF
_2rda
490 1 _aAdvances in Experimental Medicine and Biology,
_x0065-2598 ;
_v642
505 0 _aThe Sarcomere and Sarcomerogenesis -- Skeletal Muscle Alpha-Actin Diseases -- Nebulin-A Giant Chameleon -- Skeletal Muscle Disease Due to Mutations in Tropomyosin, Troponin and Cofilin -- Investigations into the Pathobiology of Thin-Filament Myopathies -- Mouse Models for Thin Filament Disease -- Thick Filament Diseases -- Acute Quadriplegic Myopathy: An Acquired "Myosinopathy" -- Third Filament Diseases -- The Z-Disk Diseases -- Intermediate Filament Diseases: Desminopathy -- Muscular Integrity-A Matter of Interlinking Distinct Structures via Plectin -- The Sarcomere and the Nucleus: Functional Links to Hypertrophy, Atrophy and Sarcopenia -- Other Model Organisms for Sarcomeric Muscle Diseases -- Therapeutic Approaches for the Sarcomeric Protein Diseases.
520 _aAlthough best known for its role in heart disease, the sarcomere--the fundamental unit of muscle contraction--is also involved in skeletal muscle diseases. Chapters in The Sarcomere and Skeletal Muscle Disease provide an up-to-date review of diseases caused by mutated proteins in the different sub-compartments of the sarcomere, document the techniques currently being used to investigate the pathobiological bases of the diseases, which remain largely unknown, and discuss possible therapeutic options.
650 0 _aMEDICINE.
650 0 _aHUMAN PHYSIOLOGY.
650 1 4 _aBIOMEDICINE.
650 2 4 _aBIOMEDICINE GENERAL.
650 2 4 _aHUMAN PHYSIOLOGY.
710 2 _aSpringerLink (Online service)
773 0 _tSpringer eBooks
776 0 8 _iPrinted edition:
_z9780387848464
830 0 _aAdvances in Experimental Medicine and Biology,
_x0065-2598 ;
_v642
856 4 0 _uhttp://dx.doi.org/10.1007/978-0-387-84847-1
_zVer el texto completo en las instalaciones del CICY
912 _aZDB-2-SBL
942 _2ddc
_cER
999 _c59228
_d59228